World J Pediatr Congenit Heart Surg. 2016 Sep;7(5):651-4. doi: 10.1177/2150135116656979. Epub 2016 Aug 12.
Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome.
Author information
- 1. Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
- 2. Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA, visiting student from The Jikei University School of Medicine, Tokyo, Japan.
- 3. Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA nhibino1@jhmi.edu.
Abstract
Loeys-Dietz syndrome (LDS) is an autosomal dominant genetic connective tissue disorder associated with aortic aneurysmal disease. Kommerell diverticulum (KD) is a rare aortic diverticulum, for which the indication for surgery and the surgical techniques remain subjects of debate. We describe our experience with a successful total aortic arch replacement including KD resection through a median sternotomy for a pediatric patient with LDS.
© The Author(s) 2016.
KEYWORDS:
Kommerell diverticulum; Loeys-Dietz syndrome; aberrant right subclavian artery; congenital heart disease
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